/library/oar/handle/123456789/3649 2025-11-13T11:53:36Z /library/oar/handle/123456789/4300 Title: Pulmonary valvulotomy in a fetus with pulmonary atresia with intact ventricular septum : first experience in Turkey Authors: Polat, Tugcin Bora; Danısman, N. Abstract: The mortality and morbidity of children with pulmonary atresia with intact ventricular septum (PA/IVS) is closely related with right ventricle hypoplasia and its consequent hemodynamics. Prenatal intervention for fetuses with PA/IVS has the potential to improve growth of the RV and the prospect of a biventricular outcome after birth. Successful valvulotomy of the pulmonary valve (PV) was performed in a fetus with PA/IVS at 28 weeks. Following the procedure there was an improvement in fetal hemodynamics. In utero perforation and dilation of the PV in midgestation fetuses with PA/IVS is technically feasible. The initial results are promising and may be associated with improved right heart growth and postnatal outcome. 2012-01-01T00:00:00Z /library/oar/handle/123456789/4285 Title: Gastric pseudoaneurysm in the setting of Loey’s Dietz Syndrome Authors: Likes, Maggie L.; Johston, Troy Alan Abstract: Loey’s Dietz syndrome is a disorder of connective tissue caused by a mutation in the genes that encode transforming growth factor (TGF) beta receptor 1 and 2. It is an autosomal dominant disorder similar to Marfan’s syndrome but with a more aggressive clinical course. Patients with Loey’s-Dietz syndrome have progressive dilatation of the aortic root that can lead to aortic dissection and rupture. The location of non-aortic arterial aneurysms may be wide spread but often occur in the head and neck vessels. 2012-01-01T00:00:00Z